fabry相关论文
Implantable image sensors have the potential to revolutionize neuroscience. Due to their small form factor requirements;......
Anderson-Fabry disease presenting with atrial fibrillation as earlier sign in a young patient:A case
BACKGROUND Anderson-Fabry disease(AFD)is an X-linked lysosomal storage disorder that results from a deficiency ofα-gala......
本文报道一例女性Ｆａｂｒｙ氏病的肾脏超微结构表现。该病人除了持续性蛋白尿外，无其它临床症状。电镜下见肾小球脏层上皮细胞胞质内充满嗜锇......
Fabrication of optical fiber sensor based on double-layer SU-8 diaphragm and the partial discharge d
In this paper, a partial discharge detection system is proposed using an optical fiber Fabry-Perot(FP) interferometric s......
绒毛采样技术的推广,使许多代谢性疾病能在妊娠头三个月进行产前诊断,但至今尚无关于Fabry′s病的报告。 Fabry′s病是由于缺乏α......
Fabry’s病为一罕见的伴性遗传性全身性疾病,是临床上唯一神经症状不显著的中枢神经系统鞘脂类沉积症、特征性皮疹、青春期闪电样......
Fabry病是先天缺乏α-半乳糖甙酶A所引起的糖脂代谢异常性疾病。临床表现为全身多发性表皮角化性血管瘤,四肢末梢神经痛,出汗障碍......
Fabry病,又称为弥漫性躯体血管角皮瘤(angiokeratoma corporis diffusum,ACD)是一罕见的伴性隐性遗传性神经皮肤综合征,国内仅有5......
Ｆａｂｒｙ病陈惠萍曾彩虹朱茂艳关键词Ｆａｂｒｙ病遗传肾活检中图法分类号Ｒ５９６２１病例报告患者男性，２０岁，因出汗减少１６年，指趾疼痛，腰背部红色皮疹１０年，发现蛋白尿７个月......
患者，男性，２１岁，因皮疹７年，发现蛋白尿两个月于１９９８年５月６日入院。患者于７年前无明显诱因出现全身皮疹，皮疹呈点状无压痛、不痒，但逐年增多。２个月前......
Fiber in-line Fabry–Pérot interferometer for simultaneous measurement of reflective index and temper
A fiber in-line Fabry–Pérot interferometer is presented. The sensing head consists of a micro ellipsoidal air cavity a......
据《N Eng1 J Med》2001年345卷第1期报道 法布里(Fabry’S)病为溶酶体α-半乳糖苷酶A缺乏症,由于N-脂酰鞘氨醇三己糖苷(globotri......
目的 报道 2个Fabry病家族的临床及病理特点 ,讨论血管改变对疾病发展的影响。方法 2例先证者均为男性患儿 ,以发作性肢端疼痛......
We present here the course of clinical response of a 53-yearold haemodialysed Fabry patient who received recombinant hum......
A single sheet of graphene exhibits the ability to turn polarization of light by several degrees in modest magnetic fiel......
研制成以ＬｉＮｂｏ３质子交换光波导Ｆ－Ｐ型干涉调制器阵列为核心结构的电光模数转换器。简述了Ｆ－Ｐ型模数转换器的原理，报导了实验样品的设计参数、制备......
法布莱(Fabry)病是一种罕见的x连锁隐性遗传的α-半乳糖苷酶A缺乏导致致糖苷神经鞘脂类成分堆积于组织器官引起的多系统疾病,Fabry......
目的对一个临床表现酷似肥厚型心肌病的FABRY病家系进行Α半乳糖苷酶(ΑGALA)基因测序并发现其突变形式。方法该家系成员共15例,经......
本文提出了一种孤子源非线性啁啾的模型，利用解析和计算机模拟的方法从理论上分析了孤子源啁啾，特别是非线性啁啾对孤子传输的影响，并......
An all optical all fiber optical bistability operation has been realized in an all fiber cavity consisted with Er do......
The wavelength tuning ranges of a grating external-cavity laser diode (ECLD) have been studied by the equivalent cavity ......
A high sensitivity fiber Bragg grating pressure sensor by using mechanical amplifier is demonstrated. The measured press......
研究了Ｆ－Ｐ型解复用器在密集波分复用系统中引入的信道间串扰对系统的影响。理论上分别建立了Ｆ－Ｐ的信道串扰模型和接收机的误码率模型，并与......
随着医学的发展和社会文明程度的提高,人们对罕见病的重视程度有了极大提高。罕见病病种繁多,各疾病临床表现多样,如不加以重视,极......
The Fabry-Perot resonator (FPR) antenna has found wide applications in microwave and millimeter waves and recently attra......
A novel extrinsic fiber-optic Fabry-Perot interferometric strain sensor system is demonstrated based on the simultaneous......
ZarlinkSemiconductor公司的长波型Fabry-Perot激光二极管是一种边缘发光器件,可沿单模光纤传送脉冲光线。它的波长为1300nm,有ZL6......
Si-based optoelectronics is becoming a very active research area due to its potential applications to optical communicat......
High power single-mode large-mode-area photonic crystal fiber laser with improved Fabry-Perot cavity
An Yb3+-doped double-clad large-mode-area photonic crystal fiber (LMA PCF) laser with 103-W single-mode continuous-wave ......
A novel time-to-live countdown scheme based on asymmetric Mach-Zehnder interferometer and Fabry-Pero
We propose a novel optical time-to-live (TTL) processing scheme using asymmetric Mech-Zehnder interferometer (AMZI) and ......
A novel scheme of label abstraction and erasion based on Fabry-Perot semiconductor optical amplifier
A novel label abstraction and erasion scheme based on a Fabry-Perot semiconductor optical amplifier (FP-SOA) is proposed......
A novel scheme of all-optical AND gate based on a Fabry-Perot semiconductor optical amplifier(FP-SOA) is proposed and it......
A strongly pumped Yb-doped large-mode-area photonic crystal fiber(LMA-PCF)laser is analyzed.The lasing characteristics o......
A photonic crystal fibre Brillouin laser based on fibre Bragg grating Fabry-Perot cavity is presented.A highly nonlinear......
The collected spectrum of the fiber Bragg grating(FBG) and the loss of the detected optical power are discussed with res......
The characteristics of transmission spectra for the all fiber,multi-cavity FabryPerot(FP) configuration based on fiber B......
The master laser of an injection-seeded laser for Doppler wind lidar is frequency stabilized to a Fabry- Perot(FP)cavity......
分析了基于光纤光栅的全光纤型双腔Fabry-Perot(F-P)结构传输谱特性.理论推出了两腔F-P结构传输率具体计算公式,给出在光栅中心波......
Influence of laser linewidth on external-cavity frequency doubling efficiency of a 1.56 μm master os
By using an external-cavity frequency-doubling master oscillator fiber power amplifier (MOPA), a 700 mW continuous-wave ......
External-cavity birefringence feedback effects of microchip Nd:YAG laser and its application in angl
External-cavity birefringence feedback effects of the microchip Nd:YAG laser are presented.When a birefringence element ......
Measurement of refractive index modulation on PMMA/E49/TNF/ECZ polymer-dispersed liquid crystal by f
The fiber Fabry-Perot interferometer used to measure the refractive index modulation of polymer-dispersed liquid crystal......
A high-efficiency Brillouin fiber ring laser is demonstrated using the standard single-mode fiber.The laser exhibits a 3......
Modulation response performances of a Fabry-Perot semiconductor laser subjected to light injection f
The modulation response characteristics of a Fabry-Perot semiconductor laser(slave FP-LD) subjected to light injection f......
Distortion of optical feedback signals in microchip Nd:YAG lasers subjected to external multi-beam i
This paper proposes a theoretical analysis for the characteristics of an external cavity Nd:YAG laser with feedback of m......
Bidirectional radio-over-fiber systems with SSB modulation and wavelength reuse based on injection-l
A 60-GHz bidirectional radio-over-fiber (RoF) system using two-carrier-injected distributed feedback (DFB) laser is prop......
In the laser warning system, a non-mechanical scanning Fabry-Perot (F-P) type laser warning method and its crucial compo......
