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目的：研究Ｓｔｕｒｇｅ－Ｗｅｂｅｒ综合征的ＣＴ、ＭＲＩ表现特点，并评价两种检查方法的诊断价值。材料与方法：回顾分析９例Ｓｔｕｒｇｅ－Ｗｅｂｅｒ综合征的临床及影像学资料。全部病例均有面部三叉神经分布区皮肤血管瘤以及同侧颅内相关的病理改变。经ＣＴ检查６例，ＭＲＩ检查３例。结果：ＣＴ、ＭＲＩ显示患侧皮层钙化９例，脑萎缩７例，侧室脉络丛增大３例，颅盖板障增厚５例。增强ＣＴ显示脉络丛明显强化２例，钙化灶周围脑回状强化１例。ＭＲＩ显示侧室脉络丛增大及室管膜下静脉扩张１例。结论：ＣＴ和ＭＲＩ能有效地发现Ｓｔｕｒｇｅ－Ｗｅｂｅｒ综合征的颅内病理改变。在显示皮层钙化灶的存在和范围上，ＣＴ优于ＭＲＩ。但在显示脑实质的其他异常，软脑膜血管瘤畸形和伴发的血管性异常方面，ＭＲＩ则优于ＣＴ。
Objective: To study the CT and MRI features of Sturge-Weber syndrome and to evaluate the diagnostic value of the two methods. Materials and Methods: The clinical and imaging data of 9 cases of Sturge-Weber syndrome were retrospectively analyzed. All patients had facial trigeminal nerve distribution of cutaneous hemangiomas and ipsilateral intracranial pathological changes. The CT examination in 6 cases, MRI examination in 3 cases. Results: CT and MRI showed ipsilateral cortical calcification in 9 cases, brain atrophy in 7 cases, lateral choroid plexus enlargement in 3 cases, and cranial platelet thickening in 5 cases. Enhanced CT showed significant enhancement of the choroid plexus in 2 cases, 1 case of calcification around the brain back enhanced. MRI showed an increase of lateral choroid plexus and subventricular vena cava dilatation in 1 case. Conclusion: CT and MRI can effectively detect intracranial pathological changes of Sturge-Weber syndrome. CT is superior to MRI in showing the presence and extent of cortical calcifications. However, MRI is superior to CT in terms of other abnormalities that manifest brain parenchyma, pial aneurysm malformations, and associated vascular abnormalities.