肾上腺髓样脂肪瘤是一种临床很少见的良性无功能性肾上腺肿瘤，由不同比例的脂肪和骨髓成分构成，文献中报告本病少于３００例，其中手术切除者仅１００余例。本文综合文献，对本病作一系统介绍。 Adrenal myeloid lipoma is a benign nonfunctional adrenal tumor that is rarely seen in clinical practice. It is composed of different proportions of fat and bone marrow components. In the literature, less than 300 cases of this disease have been reported, of which only 100 cases have undergone surgical resection. This article provides a systematic introduction to the disease.