原发性下腔静脉平滑肌肉瘤(primary leiomyosarcoma of the inferior vena cava,PIVCLMS)比较罕见,多数见于女性,常因症状不典型而易被误诊,术前明确诊断常须CT联合下腔静脉(IVC)造影。随着影像学技术尤其血管外科技术的提高,使得该病得以早期诊断并及时得到治疗。我院近期收治PIVCLMS病人2例,结合文献报告如下。1临床资料 Primary leiomyosarcoma of the inferior vena cava (PIVCLMS) is relatively rare, most found in women, often due to atypical symptoms and easily misdiagnosed, preoperative diagnosis of CT often associated with inferior vena cava (IVC) Contrast With the improvement of imaging technology, especially vascular surgery, the disease can be diagnosed early and treated promptly. Recently admitted to our hospital PIVCLMS patients 2 cases, combined with the literature report is as follows. 1 clinical data