邬××,男,50岁,已婚,工程师。患者14岁起即发现两眼视力差伴耳聋,并逐渐加重,于1983年7月9日来我科门诊,要求验光配镜。父母非近亲结婚,家族中无类似疾病者。眼部检查:右眼光感。左裸眼视力0.3,近视力0.8,-1.00球(?)-1.50柱×90轴=0.8。内眥距离33毫米。睑裂宽度:右眼10毫米;左眼8毫米。右眼外斜15°(角膜映光法)。双眼睑、球结膜及角膜正常。左眼前房深度正常,右眼颞侧较鼻侧为深。房水均清。 Wu XX, male, 50 years old, married, engineer. The patient was found to have poor visual acuity with deafness at 14 years of age and gradually increased. He came to our clinic on July 9, 1983 and asked for optometry. Parents are married to non-relatives and have no similar illnesses in the family. Eye examination: Right eye light sense. Left uncorrected visual acuity 0.3, near vision 0.8, -1.00 ball (?) - 1.50 x 90 axis = 0.8. Internal 眦 distance 33 mm. Palpebral fissure width: right eye 10 mm; left eye 8 mm. Right eye oblique 15 ° (corneal reflection method). Double eyelid, conjunctival and corneal normal. Left anterior chamber depth normal right temporal eye than the nasal deep. Room water are clear.