神经鞘膜组织的良性肿瘤与其它间叶性肿瘤一样,具有非常明显的异质性。直至不久前,才将不呈许旺氏瘤及神经纤维瘤组织模式的大多数肿瘤,定名为良性周围神经鞘瘤。这组来源不同的肿瘤包括形态不同的、呈神经分化的肿瘤。因其部分地在生物学和预后方面有所不同,故有必要加以了解,以避免误诊为可能有侵犯性的恶性肿瘤。借助免疫组化和电镜观察, The benign tumors of the nerve sheath, like other mesenchymal tumors, have very distinct heterogeneity. Until recently, most tumors that did not exhibit Schwann’s tumour and neurofibroma tissue patterns were designated as benign peripheral nerve sheath tumors. This group of tumors from different sources includes morphologically different, neurally differentiated tumors. Because of its differences in biology and prognosis, it is necessary to understand it in order to avoid misdiagnosis as a potentially malignant tumor. With immunohistochemistry and electron microscopy,