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视网膜色素变性(RP)是一种较常见的致盲眼病。1981年美国RP 国家基金会主持召开的关于RP 术语和检查方法的专题讨论会认为本病是弥漫性地主要侵犯光感受器和影响色素上皮功能的一组进行性遗传性疾病。本病致盲率高且具有遗传性,至今又无有效的治疗方法,因此,加强其理论和临床的研究实属必要。为了探讨RP 的临床规律、RP 的遗传及影响预后的因素,以便为研究本病的病因、发病机理及防治方法提供和积累临床资料。本文对62例经全视野ERG检查确诊的原发性RP 患者进行了临床分析。
Retinitis pigmentosa (RP) is a more common cause of blindness. The symposium on RP terminologies and examination methods hosted by the RP National Foundation in 1981 in 1981 considered the disease to be a group of progressive hereditary diseases that mainly diffusely affect photoreceptors and affect the function of the pigment epithelium. The blinding of the disease is high and hereditary, so far no effective treatment, therefore, to strengthen its theoretical and clinical research is necessary. In order to explore the clinical rules of RP, the inheritance of RP and the prognostic factors in order to provide and accumulate clinical data for studying the etiology, pathogenesis and prevention and treatment of this disease. In this paper, 62 cases of primary RP diagnosed by full-field ERG examination were analyzed.