作者报道了伴有独特的血管平滑肌瘤样增生性间质的肾透明细胞癌。5例均为会诊病例,女性4例,男性1例,年龄37~75岁(平均53岁),4例位于右侧肾脏,1例位于左侧,3例有血尿,除1例因乳腺癌行双侧乳房切除术外无明显过去史,均无结节性硬化的临床症状,4例行部分肾切除术,1例行全肾切除术, The authors report on clear cell renal carcinoma with a unique vascular leiomyoma-like proliferative stroma. 5 cases were diagnosed, 4 were female, 1 male, aged 37 to 75 years (mean 53 years), 4 in the right kidney, 1 in the left, 3 with hematuria, except for 1 case of breast cancer Line bilateral mastectomy without obvious past history, no clinical symptoms of tuberous sclerosis, 4 cases of partial nephrectomy, 1 case of radical nephrectomy,