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目的了解偏侧萎缩症的临床特点、病理组织学和超微结构改变。方法对1例单纯右下肢萎缩患者的临床表现、实验室检查、组织病理学及超微结构进行分析。结果患者右下肢皮肤变薄,皮下组织几乎消失,肌肉轻度萎缩,骨骼变短,神经系统检查和相关实验室检查均无异常,患肢皮肤和肌肉活检在光镜下见肌纤维散在萎缩,肌膜炎性细胞浸润,血管壁明显增厚,管腔狭窄,皮肤各层组织变薄,皮下脂肪组织减少;电镜下见在有病变的肌纤维内线粒体减少并空泡样变,肌细胞胞核数目减少,胞核周围胞浆内可见异常颗粒沉积。结论单纯一个肢体萎缩可能是偏侧萎缩症的一个特殊类型。
Objective To understand the clinical features, histopathology and ultrastructural changes of hemiplegia. Methods The clinical manifestations, laboratory tests, histopathology and ultrastructure of 1 patient with right lower extremity atrophy were analyzed. Results The skin of the right lower extremity was thinned, the subcutaneous tissue almost disappeared, the muscle was mildly atrophied, the bones shortened, and the neurological examination and related laboratory examination showed no abnormalities. The skin and muscle biopsies of the affected limbs were seen scattered and atrophied in the light microscope. Membranous inflammatory cell infiltration, vascular wall thickening, narrow stenosis, the skin tissue thinning, subcutaneous adipose tissue decreased; electron microscopy in the lesion of the mitochondrial mitochondria and vacuolar degeneration, the number of myocytes nuclei Reduce the abnormal cytoplasm deposition in the cytoplasm around the nucleus. Conclusion A mere limb atrophy may be a special type of hemiplegia.