遗传性胃肠道息肉病伴粘膜皮肤色素沉着症也称为黑色素斑-胃肠道多发性息肉综合征或皮-杰氏(Peutz-Jeghers)综合征.这是一种少见的常染色体显性遗他性疾病,其临床特点是口唇和口腔颊粘膜及肢体末端皮肤有黑色素沉着、胃肠道多发性错构瘤性息肉病.现将我们近年遇到的4例报告如下.例1:周某,男,21岁.主诉剑突下隐痛,曾 Hereditary gastrointestinal polyposis with mucocutaneous pigmentation is also known as melanoma - polyposis in the gastrointestinal tract or Peutz-Jeghers syndrome, a rare autosomal dominant Hereditary diseases, the clinical features of the lips and buccal mucosa and extremities of the skin with melanin, gastrointestinal multiple hamartoma polyposis. Now we encountered in 4 cases reported as follows. Example 1: Week A, male, 21 years old complained of xipong pain, had