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低钾型远端肾小管性酸中毒因缺乏肾脏疾病常有的特异性,往往容易误诊或漏诊。本文报道8例如下。临床资料1.一般资料:本文8例均根据下列依据确诊:①代谢性酸中毒而尿pH>6.5;②低血钾、软瘫或肌无力;③氯化铵负荷试验尿pH仍>5.5。8例中女6例,男2例。年龄16~36岁,平均28.63±8.15岁。病程10天~4.5年。病因:慢性棉酚中毒2例,慢性乙型病毒性肝炎2例,慢性肾盂肾炎1例,原因不明3例。
Hypokalemic distal renal tubular acidosis due to the lack of specificity of kidney disease often tend to be misdiagnosed or missed diagnosis. This article reports 8 cases as follows. Clinical data 1. General information: The 8 cases were diagnosed on the basis of the following: ① metabolic acidosis and urine pH> 6.5; ② hypokalemia, soft or paralysis or muscle weakness; ③ ammonium chloride load test urine pH> 5.5. 8 cases of female 6 cases, 2 males. Age 16 to 36 years, mean 28.63 ± 8.15 years. Duration of 10 days ~ 4.5 years. Etiology: chronic gossypol poisoning in 2 cases, 2 cases of chronic hepatitis B, chronic pyelonephritis in 1 case, unknown cause in 3 cases.