婴儿多囊肾伴多囊肝属常染色体隐性遗传病。我院自1988年至1991年共通4例，其中1例为连续3胎，1例为连续2胎患同一疾病。现将4例临床及尸解情况报告如下。临床资料一、一般资料男2例为同胞，女2例。二、临床表现2例男婴生后即亡，2例女婴为死产。病理解剖一、巨检4例主要畸形为 Polycystic kidney disease with polycystic liver disease is autosomal recessive disease. Our hospital from 1988 to 1991 a total of 4 cases, of which 1 case of 3 consecutive pregnancies, 1 case of 2 consecutive pregnancies suffering from the same disease. Now 4 cases of clinical and autopsy are as follows. Clinical data First, the general information Male 2 cases of siblings, 2 females. Second, the clinical manifestations of 2 male infants died immediately after birth, 2 female infant births. Pathological anatomy First, the 4 cases of major deformity as