原发性巨输尿管症系胚胎期输尿管发育畸形，为泌尿系统少见疾病。本病无典型临床症状和体症，以输尿管末段功能性狭窄，其上部明显扩张为主要特征。国内、外报道尚不多见［１］。作者对１０例患者的尿路造影表现，综合文献复习做一回顾性分析。１临床资料１．１一般资料１... Primary giant ureter of embryonic ureter developmental deformity, urinary system is a rare disease. The disease without typical clinical symptoms and physical illness, functional distal stenosis ureter, the upper part of the obvious expansion as the main feature. Domestic and foreign reports are rare [1]. The author of 10 patients with urography, comprehensive review of the literature to do a retrospective analysis. 1 clinical data 1.1 general information 1 ...