纤维囊性变患儿伴有胰腺结构破坏。本病的特点是胰腺外分泌功能不足,同时内分泌也受影响,但很少并发明显的糖尿病和酮症。口服葡萄糖后内源性胰岛素的释放明显减少,但高血糖一般不重,并且病人对外源性胰岛素敏感。作者对7名纤维囊性变病人的糖 Fibrous cystic change in children with pancreatic damage. The disease is characterized by inadequate pancreatic exocrine function, while endocrine is also affected, but rarely complicated by significant diabetes and ketosis. After oral glucose release of endogenous insulin was significantly reduced, but high blood sugar is generally not heavy, and the patient is sensitive to exogenous insulin. The author of seven patients with cystic fibrosis of the human sugar