一、全身性有痛性肌痉挛1963年吉里最初报告一个新的综合征——全身性有痛性肌痉挛,以后有人提倡称为吉里氏病。现在由于其病理生理和病理解剖已基本明确,吉里本人建议,称本综合征为“进行性肌痉挛、脱鬟、腹泻综合征(a syndromeof progressive muscle spasm alopecia anddiarrhoea)”,现在认为这是一种特异的“吸收障碍综合征”。本病的特征是10岁左右发病,女性多见。有进行性的有痛性的间歇性肌痉挛,肌痉挛最初多发于下肢肌,伴发剧烈疼痛,数年内向臀肌、腹肌、上肢各肌扩延,5～6年后甚至颈肌、颞肌、咬肌也受累。同时发生脱发脱毛、无月经等内分泌障碍,腹泻及吸收障碍引起的糖代谢 First, the systemic pain muscle spasm Jiri in 1963 initially reported a new syndrome - systemic pain muscle spasm, was later advocated as called Kyrgyzstan’s disease. Now because of its pathophysiology and pathological anatomy has been basically clear, Jiri himself suggested that the syndrome is “progressive muscle spasm, drooping, diarrhea syndrome (a syndrome of progressive muscle spasm alopecia and diarrhea)”, now that this is a Specific “malabsorption syndrome.” The characteristics of the disease is about 10-year-old onset, more common in women. There are progressive painful intermittent muscle spasm, muscle spasm initially in the lower limb muscle, accompanied by severe pain, a few years to the gluteal muscle, abdominal muscles, upper limb muscle extension, 5 to 6 years after the neck or even muscle, Temporal muscle, masseter muscle involvement. At the same time hair loss hair removal, no menstrual endocrine disorders, diarrhea and absorption disorders caused by glucose metabolism