肾恶性横纹肌样瘤是一罕见的高度恶性肿瘤,临床、CT和病理表现均有特殊之处。本文报告2例,均经病理诊断。作者认为肾脏广泛破坏,形成以囊性变为主并存“溶冰状”改变的软组织肿块,累及肾盂、伴肾包膜侵袭结节和肾包膜下积液是本病的CT特点。 Malignant rhabdomyosarcoma is a rare and highly malignant tumor with clinical, CT and pathological findings. This article reports 2 cases, both by pathological diagnosis. The authors believe that the extensive destruction of the kidneys, the formation of cystic degeneration coexist “ice-like” changes in soft tissue mass, involving the renal pelvis, with renal capsule invasion nodules and renal capsule effusion is the CT features of the disease.