本病又名UIlrch-Fremerey-Do-hna氏综合症,或称Francois氏综合症或llearmann-Streiff氏症。本症是一种罕见的疾患,由胚胎5-7周额叶发育障碍所致。无染色体异常,可能为常染色体隐性遗传,发病可能与畸胎物质或病毒感染有关。常为家族性发病或双亲为血族联姻者。目前在国内报导较少,我区尚未见到病例报告,我院于1982年6月至11月间发现两例,现报告如下。病例报告例一:程××女性 15岁汉族 This disease is also called UIlrch-Fremerey-Do-hna’s syndrome, or Francois’s syndrome or llearmann-Streiff’s syndrome. This disease is a rare condition caused by embryonic developmental disorders of the frontal lobes 5-7 weeks. No chromosomal abnormalities may be autosomal recessive, the incidence may be related to teratogenic substances or viral infection. Often for familial onset or parents of kinship marriage. At present, there are few reports in our country and no case report has been seen in our district. Two cases were found in our hospital from June to November 1982, and the report is as follows. Case Report Case 1: Cheng × × female 15-year-old Han nationality