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作者报告一例Down综合征合并系统性红斑狼疮(SLE)。患者为20岁白人女性,患Down综合征、先天性心脏病和怀疑的Eisenmenger综合征伴肺动脉高压。1981年8月因充血性心衰而住院,体温达39℃,持续不退,多次血培养阴性,1981年11月逐渐出现多关节疼痛和肿胀。检查发现两侧近端指间关节、掌指关节、腕、肘、踝和距跟关节肿胀,并有轻度尺侧偏斜,两肘屈曲挛缩,两肩活动受限,两膝关节有渗出,蹠趾关节压痛,颧部持续红斑和片状脱发,
The authors report a Down syndrome with systemic lupus erythematosus (SLE). The patient is a 20-year-old Caucasian woman with Down syndrome, congenital heart disease and suspected Eisenmenger syndrome with pulmonary hypertension. 1981 August due to congestive heart failure and hospitalization, body temperature of 39 ℃, sustained remission, blood culture many negative, in November 1981 gradually multi-joint pain and swelling. Examination found that the proximal interphalangeal joints on both sides, metacarpophalangeal joint, wrist, elbow, ankle and heel joint swelling, and mild ulnar deviation, flexion contracture of two elbows, both shoulders limited mobility, both knee seepage Out, metatarsophalangeal joint tenderness, erythema and lamellar hair loss continued,