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目的探讨腹内型韧带样型纤维瘤病(DF)的CT表现。方法搜集4例经手术病理证实的腹内型DF的临床及影像资料,均行CT平扫及多期增强扫描,结合文献回顾性分析其CT特征。结果 4例均为单发病变,分别位于小肠系膜、回结肠系膜、大弯侧胃壁、肝脏;均呈类圆形或分叶状软组织肿块,轮廓清晰,体积较大,最大径线8.0~15.0 cm,平均10.3 cm;平扫时3例相对骨骼肌呈均匀低密度,增强扫描呈渐进性、不均质、轻-中度强化;1例相对肝实质呈混杂略低密度,内见斑片状更低密度区,动脉期片絮状明显强化,门静脉期及延迟扫描呈持续强化,强化范围逐步扩大,强化区密度均匀,夹杂有裂隙状低密度区。结论腹内型DF的CT表现具有一定的特征性,可提示诊断,确诊仍需病理及免疫组织化学证实。
Objective To investigate the CT findings of intra-abdominal ligament-like fibromatosis (DF). Methods The clinical data and imaging data of 4 cases of intra-abdominal DF confirmed by pathology were collected. Both CT scan and multi-phase enhanced scan were performed. The CT features were retrospectively analyzed. Results Four cases were single lesion, located in the small mesentery, the mesentery on the mesocolon, the stomach wall at the greater curvature and the liver, all showed round or lobulated soft tissue mass with clear outline and larger volume, 15.0 cm, an average of 10.3 cm; 3 cases of plain skeletal muscle showed a uniform low density, enhanced scan was progressive, heterogeneous, mild to moderate enhancement; 1 case of relative liver parenchyma mixed slightly lower density, More low-density sheet area, arterial floc was significantly enhanced, portal vein and delayed scan was continued to strengthen the gradual expansion of the scope of strengthening the uniform density, mixed with crack-like low-density areas. Conclusion The CT findings of intra-abdominal DF have certain characteristics, which may indicate the diagnosis and confirmation of pathology and immunohistochemistry.