原发性小血管炎主要指韦格纳肉芽肿病(We gener’sgranulo -matosis) ,显微镜多血管炎(micro scopicpolyangiitis)和局灶节段坏死性肾小球肾炎。此病为系统性自身免疫性疾病,可累及全身多个脏器。其中肾脏受累明显并进展迅速,肺部受累病情亦凶险,及时诊断和治疗非常重要,现将我 Primary small vasculitis mainly refers to Wegener’s granulomatosis, micro-scopic polyangiitis, and focal segmental necrotizing glomerulonephritis. The disease is a systemic autoimmune disease that can affect multiple organs throughout the body. Including renal obvious and rapid progress, lung involvement disease is dangerous, timely diagnosis and treatment is very important, now I