原来认为肾恶性横纹肌瘤是Wilms瘤的一种肉瘤变异,现在则认为在临床及病理特征方面是两个不同的病种,作者报导2例。例1,男,7个月。因呕吐、低热、震颤入院,右上腹触及一大的肿块,US示右肾有一9cm大小实质肿块伴周围有大量积液。CT示软组织肿块源自右肾并压迫正常肾实质,还见一大的低衰减积液,包膜下间隙中有 It was originally thought that renal malignant rhabdomyosarcoma is a sarcoma mutation of Wilms tumor, and now it is considered in clinical and pathological features are two different diseases, the authors reported in 2 cases. Example 1, male, 7 months. Due to vomiting, fever, tremor admission, the right upper quadrant touching a large lump, the US shows the right kidney has a mass of 9cm with a large mass of effusion around the body. CT showed soft tissue mass from the right kidney and oppression of normal renal parenchyma, also see a large low-loss effusion, subgapsal space