我院近期收治1例马蹄肾伴右重复肾并右下肾积水患者。泌尿系统二种较罕见的先天性发育畸形合并于一身,在临床上实属罕见,现报告如下。患者,男,40岁。因右腰胁部胀痛伴低热、脓尿月余。在当地医院检查尿常规脓细胞+++.按泌尿系炎症治疗服抗生素3周,症状略有缓解,转我院复诊。门诊 B 超仅提示右肾积水,但原因不明而收治入 In our hospital recently admitted to a case of horseshoe kidney with right kidney and right lower kidney hydronephrosis patients. Urinary system, two rare congenital malformations combined in one, is clinically rare, are as follows. Patient, male, 40 years old. Due to the right lower back pain with low fever, pyuria and more than a month. Urine routine examination of pus in local hospitals +++. Press urinary tract inflammation treatment of antibiotics for 3 weeks, the symptoms were slightly relieved, referral to our hospital. Out-patient B-only prompted the right hydronephrosis, but the reasons for admission and admitted