原发性脑脊髓膜恶性黑色素瘤属于斑痣性错构瘤[ 1] ，大约30%的病例合并皮肤的有毛痣。国内仅见数例报道，现将我们遇到的1 例报告如下。1 病例介绍患者男，15 岁，主诉因间歇性肢体抽搐40 余天，逐渐加重入院。既往无外伤、手术史、否认家族遗传性疾病病史。查体：一般情况较 Primary meningioma of the brain is a meningioma hamartoma [1], about 30% of cases combined with hairy mole of the skin. Only a few cases reported in China, we now encounter a case report is as follows. 1 case description Male patient, 15 years old, complained of intermittent limb twitch more than 40 days, gradually increased admission. No previous trauma, surgery history, deny the family history of genetic disease. Physical examination: the general situation is more