本文报道在北京地区发现的一例经血红蛋白化学结构分析证实的HbE复合β~+地中海贫血(以下简称β地贫)。先证者,女2~+岁,汉族,北京市人,具有严重贫血、肝牌肿大等β地贫典型症状。先证者的血红蛋白4.6克％红细胞278万/mm~3红细胞大小 This article reports a case of HbE complex β ~ + thalassemia (hereinafter referred to as β thalassemia) confirmed by chemical structure analysis of hemoglobin in Beijing. The proband, female 2 ~ + years old, Han nationality, Beijing city people, with severe anemia, liver enlargement and other β thalassemia typical symptoms. Probability of the hemoglobin 4.6 grams of red blood cells 2.78 million / mm ~ 3 red blood cell size