先天性单纯性肺动脉狭窄为临床上比较多见的先天性心血管畸形之一,过去许多临床工作者把这种畸形认为是一种罕见的疾病,而认为多合并室间隔缺损即法鲁氏四联症,或合并房间隔缺损即法鲁氏三联症共同存在,晚近自心脏导管检查术广泛应用于临床,以及肺动脉瓣切开术开展以后,本病的发现已逐渐的加多起来,据国内外文献资料报导,本病的发病率约占各类先天性心血管畸形的8—18％,如wood氏统计占18％,Campbell氏统计占 Congenital simple pulmonary stenosis is clinically more common one of congenital cardiovascular malformations, many clinicians in the past that the deformity as a rare disease, and that the multiple combined ventricular septal defect that Faruqiju Associated disease, or combined atrial septal defect that is common law of Farozoan triad, lately since cardiac catheterization is widely used in clinical and pulmonary valvulotomy, the discovery of the disease has gradually increased, according to the domestic Foreign literature, the incidence of this disease accounts for about 8-18% of all types of congenital cardiovascular malformations, such as Wood’s statistics accounted for 18%, Campbell’s statistics accounted for