镰状细胞病患儿左心室肥厚和舒张期功能不全与睡眠和觉醒时氧不饱和相关

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过早死亡和心脏功能不全在镰状细胞病(sicklecell disease,SCD)患者中已有描述,但其中的机制还未被完全阐明。该研究试图验证SCD患儿的心脏异常和睡眠时的异常呼吸相关这一假说。征集SCD患儿44例[平均年龄10.1(4.0~18.0)岁]进行观察研究。在患儿被纳入研究7d之内,进行常规和组 Premature death and cardiac insufficiency have been described in patients with sickle cell disease (SCD), but the mechanisms therein have not yet been fully elucidated. The study sought to validate the hypothesis that cardiac abnormalities in children with SCD are associated with abnormal breathing during sleep. Forty-four children with SCD [mean age 10.1 (4.0 to 18.0) years] were enrolled in the study. Children were included in the study within 7d, routine and group
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