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病态窦房结综合征(SSS)和先天性心脏病房间隔缺损(ASD)有遗传因素和环境因素。本文对一家系调查发现SSS为心脏先天性传导系统缺陷的外显病变,而ASD为并随性状,均和遗传有关,现报告如下。先证者(Ⅲ_4)男,5岁,ASD患者。3个月前ASD修补术。术后发热,心律不齐,经治疗体温下降,心率由88次/分降到44次/分。心电图示窦性心动过缓,窦性静止,不完全性房室脱节,房室交界性逸
Sick sinus syndrome (SSS) and congenital atrial septal defect (ASD) have genetic and environmental factors. This article on the one family survey found that SSS is an apparent pathological defect of the heart congenital conduction system, and ASD and with traits, both genetic and are reported as follows. Probable (III_4) male, 5 years old, ASD patients. ASD repair 3 months ago Postoperative fever, arrhythmia, the body temperature decreased after treatment, heart rate decreased from 88 beats / min to 44 beats / min. ECG shows sinus bradycardia, sinus quiescence, incomplete atrioventricular disconnection, atrioventricular junction