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“伴大块状淋巴结肿大的窦性组织细胞增生症” (Sinus histiocytosis with massive lymphoadenopathy)一名首先由Rosai和Dorfman(1969)提出,并认为是一新的独立疾病单元。他们报告4例,皆为儿童,主要临床表现为大块状颈淋巴结肿大、低热、白细胞增多和高丙种球蛋白血症。淋巴结肿大持续时间虽长,但呈良性经过。1972年Rosai和Dorfman又复习30例,并将34例一并总结分析。1973年Lober等及Bencroft等又发表两篇报道。
One of the patients with Sinus histiocytosis with massive lymphoadenopathy was first proposed by Rosai and Dorfman (1969) and considered as a new unit of independent disease. They reported 4 cases, all children, the main clinical manifestations of massive cervical lymph node enlargement, fever, leukocytosis and hypergammaglobulinemia. Although the duration of lymphadenopathy is long, it is benign. In 1972, Rosai and Dorfman reviewed 30 cases and summarized 34 cases. Lober et al. And Bencroft et al. Published two more articles in 1973.