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目的：分析国人多发性内分泌腺瘤的临床特征。方法：在诊断我院１例多发性内分泌腺瘤（ＭＥＮ）时，回顾性总结了国内报道的ＭＥＮ共６８例，对其病史、首发症状和年龄、临床特征、肿瘤组合、诊断方法及治疗预后进行分析总结。结果：分析显示国人各类型 ＭＥＮ比例为： ＭＥＮ－ Ⅰ型 ２２．０５％， Ⅱ型 ３６．８６％， Ⅲ型 ８．８２％，重叠型 ３３．７２％。女性多于男性（ Ｐ＜０．０５），且发病年龄较男性平均早１０岁。受累腺体多少依次为甲状腺、肾上腺髓质、垂体、甲状旁腺、胰岛。结论：国人多发性内分泌腺瘤临床特征有别于国外报道。对患甲状腺髓样癌，双侧嗜铬细胞瘤，有类马凡体型者及ＭＥＮ患者的一级血亲进行多内分泌腺的定性、定位检查是有必要的。
Objective: To analyze the clinical features of multiple endocrine adenomas in Chinese. Methods: In the diagnosis of one case of multiple endocrine adenomas (MEN) in our hospital, 68 cases of MEN reported in China were retrospectively reviewed. Their medical history, first symptoms and age, clinical features, tumor combinations, diagnosis methods and treatment prognosis were reviewed. Conduct an analysis and summary. Results: The analysis showed that the proportion of MEN of each type of people in China was: 22.05% of MEN-I type, 36.86% of type II, 8.82% of type III, and 33.72% of overlapping type. Females were more than males (P<0.05), and the onset age was 10 years earlier than males. The number of affected glands was thyroid, adrenal medulla, pituitary, parathyroid, and islet. Conclusion: The clinical features of multiple endocrine adenomas in Chinese are different from those reported abroad. It is necessary to perform qualitative and localized examination of multiple endocrine glands for patients with thyroid medullary carcinoma, bilateral pheochromocytoma, quasi-Marfan and MEN.