2007年10月,我院对1例阵发性睡眠性血红蛋白尿(PNH)患者行同基因造血干细胞移植,目前已经随访42个月,取得良好疗效,现报告如下。患者,女,18岁,因反复红茶色尿4年于2007年8月13日入我院。患者于4年前无明显诱因出现反复红茶色尿,伴面色苍白、乏力、活动后气促,曾在我 October 2007, our hospital on a case of paroxysmal nocturnal hemoglobinuria (PNH) patients with syngeneic hematopoietic stem cell transplantation, has been followed up for 42 months and achieved good results, are as follows. Patient, female, 18 years old, because of repeated black color urine 4 years in August 13, 2007 into our hospital. 4 years ago, no obvious incentive for patients with recurrent black brown urine, with pale complexion, fatigue, shortness of breath after activities, had me