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目的 分析27例烟雾病脑血管造影、CT、MRI及MRA表现。方法 脑血管造影23例,CT检查23例,MRI检查12例,MRA检查6例。结果 (1) 出现颈内动脉、大脑前动脉、大脑中动脉狭窄或闭塞及颅底异常血管网伴脑膜侧支循环分别为63% 、66.7% 、96.3% 、100% ;脑梗死、脑出血、脑萎缩及脑室扩大分别为70.4% 、14.8% 、14.8% 、18.5% 。(2) 脑血管造影、CT平扫、MRI及MRA对烟雾病的诊断率分别为100% 、0% 、50% 、100% 。结果 CT及MRI主要用于显示烟雾病的脑实质改变,而脑血管造影和MRA用于显示该病的脑血管改变。MRA是怀疑此病后首选检查方法,若患者准备手术,则需作脑血管造影进一步检查
Objective To analyze 27 cases of moyamoya disease with cerebrovascular angiography, CT, MRI and MRA. Methods Cerebral angiography in 23 cases, CT examination in 23 cases, MRI examination in 12 cases, MRA examination in 6 cases. Results (1) There were 63%, 66.7%, 96.3%, 100% incidences of internal carotid artery, anterior cerebral artery, middle cerebral artery stenosis or occlusion and abnormal cranial basement vascular network with meningeal branches, respectively. Cerebral infarction , Cerebral hemorrhage, cerebral atrophy and ventricular enlargement were 70.4%, 14.8%, 14.8% and 18.5% respectively. (2) The diagnostic rates of cerebrovascular angiography, CT scan, MRI and MRA for moyamoya disease were 100%, 0%, 50% and 100% respectively. Results CT and MRI were mainly used to show the brain parenchymal changes of moyamoya disease, while cerebral angiography and MRA were used to show the cerebrovascular changes of the disease. MRA is suspected of the disease after the preferred method of examination, if the patient is ready for surgery, you need to make further examination of cerebral angiography