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目的:探讨乳腺癌派杰氏病(Paget′s病)的流行病学、临床病理特点和预后。方法:对经手术和病理证实的8例乳腺癌派杰氏病的临床资料进行回顾性分析。结果:乳腺Paget′s病以慢性乳头皮肤改变为主要特点,平均发病年龄53岁。单纯乳腺派杰氏病4例(50%),伴有浸润性癌1例(12.5%)。总的1年和3年生存率分别为100%和87.5%,远处转移率为12.5%;触及肿块和未及肿块患者1年和3年生存率分别为100%5、0%和100%、100%;以乳头病变与乳腺肿块为首发症状患者1年和3年生存率分别为100%、100%和100%、0%;单纯Paget′s病/或合并导管内原位癌患者与Paget′s病伴有浸润性导管癌者1年和3年生存率分别为100%、100%和100%、0%。结论:乳腺派杰氏病病变局限于乳头、无可触及肿块、非浸润性癌、早期诊断及以手术为主综合治疗的乳腺癌派杰氏病患者预后较佳。
Objective: To investigate the epidemiology, clinicopathological features and prognosis of Paget’s disease in breast cancer. Methods: The clinical data of eight cases of Papillomavirus confirmed by surgery and pathology were retrospectively analyzed. Results: Paget’s disease of the breast was characterized by chronic papillary skin changes with an average age of onset of 53 years. Four cases (50%) of pure Papillomavirina and one case of invasive carcinoma (12.5%). The overall 1-year and 3-year survival rates were 100% and 87.5%, respectively, and the distant metastasis rate was 12.5%. The 1-year and 3-year survival rates were 100%, 5% and 100% for patients with or without palpable mass , 100%. The 1-year and 3-year survival rates of patients with papillary lesions and breast masses as the first symptom were 100%, 100% and 100%, 0%, respectively. Paget’s disease alone or combined with ductal carcinoma in situ The 1-year and 3-year survival rates of Paget’s disease with invasive ductal carcinoma are 100%, 100% and 100%, 0%, respectively. CONCLUSIONS: Papillary sjös disease is confined to the papillary lesion and has no palpable masses and non-invasive carcinoma. The prognosis of patients with Papillomavirus is better in the early diagnosis and surgical treatment of breast cancer.