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阵发性睡眠性血红蛋白尿症(简称 PNH)在儿科很少见,而合并何杰金氏病者更较为罕见,且两者关系不明确。现将我们在临床上见到的一例报告如下:病儿、男,13岁。因乏力,消瘦,发现脾大2年余入院。病程中有不明原因的乏力,消瘦,面色苍黄,反复不规则发热。盗汗。并有数次夜间解血红蛋白尿。在外诊断
Paroxysmal nocturnal hemoglobinuria (referred to as PNH) is rare in pediatrics, and those with Hodgkin’s disease are more common, and the relationship between the two is not clear. Now we see a clinical report as follows: Sick child, male, 13 years old. Due to fatigue, weight loss, splenomegaly found more than 2 years admitted to hospital. There are unexplained duration of fatigue, weight loss, pale yellow, repeated irregular fever. Night sweats. There are several nighttime hemoglobinuria. Out of diagnosis