病历摘要:患儿女,4岁。生后两个月时,曾因挑牙齿后牙龈出血不止,经输血后方止。此后经常出现皮肤瘀斑及鼻衄,每次长达2天多,用一般止血药效果不佳,均需输血止血。入院前8个月由发热腹泻开始反复鼻衄,经激素治疗效果不显,而 Medical history summary: children, 4 years old. Two months after birth, had bleeding gums after picking teeth more than stop after transfusion. Since then there are often skin ecchymosis and epistaxis, up to 2 days each time, with the general hemostatic effect is poor, are required to stop bleeding. 8 months before admission by fever and diarrhea began repeated epistaxis, hormone therapy is not effective, and