先天性耳前瘘管具有遗传性,但文献报道不多。作者近三年来遇到三个家系均一家三代罹患本病,且都是女性,特报告如下。家系一: 先证者,女,17岁,学生,住院号92514。因左耳先天性耳前瘘管反复感染于1981年12月14入院。患者曾在某医院先后两次行手术切除瘘管复发,入我科拟行第三次手术。术中发现瘘管向后达乳突部,长约3cm,将耳廓掀起完整切除瘘管,至今已三年无复发。经家系调查,患者同胞兄妹五人,二个哥哥健康, Congenital otic fistula with hereditary, but few reports in the literature. The author encountered in the past three years, three families were three generations of this disease, and are all women, especially the report as follows. Family A: Proof, female, 17 years old, student, hospital number 92514. Due to the left ear congenital ear fistula repeated infections in December 1981 1981 admission. Patients have twice in a hospital surgical removal of fistula recurrence, into the third line of surgery I planned. Fistula surgery found up to reach the mastoid, about 3cm, the ear set off a complete removal of fistula, has not relapsed for three years. The pedigree investigation, five siblings of siblings, two brothers healthy,