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对９例强直性肌营养不良（ＭｙＤ）患者行激发重复神经电刺激（ＡＲＮＳ）检查。１例（１１％）ＡＲＮＳ前见序列复合肌肉动作电位（ＣＭＡＰｓ）波幅递减，８例（８９％）ＡＲＮＳ后出现首位ＣＭＡＰ波幅降低，其中６例（６７％）伴序列ＣＭＡＰｓ波幅递减。首位ＣＭＡＰ波幅降低出现率和平均降低程度随病程延长而加重。认为ＭｙＤ患者的骨骼肌兴奋收缩反应减弱，可能与漫长病期致正常肌纤维数量减少及病变肌膜去极化过程减弱有关。ＭｙＤ病的波幅递减反应有别于重症肌无力
Nine patients with Myotonic dystrophy (MyD) underwent repeated excitation electrical stimulation (ARNS). The amplitude of CMAPs was decreased in 1 case (11%) ARNS, and the amplitude of CMAP was decreased after ARNS in 8 cases (89%). The amplitude of CMAPs decreased in 6 cases (67%). The first decrease in CMAP amplitude and decrease in the average extent of exacerbations with longer duration. That MyD patients with skeletal muscle excitatory contractile response weakened, may be associated with a prolonged period of normal muscle fiber to reduce the number and pathological degeneration of myofascial weakening. The amplitude-diminishing response to MyD disease is distinct from myasthenia gravis