本病属世界性分布的青壮年疾病,少见于儿童。其特点为弹性型大动脉的受累、渐进性血管炎变的加重,直至管腔的闭塞。因受累血管部位的不同,临床上常有复杂、多变、难以捉摸的表现,如早期某些缺血性症状,很易误诊为神经机能紊乱或结缔组织疾病,以导致治疗上的延误,为此,本文着重叙述了本病的临床表现、实验室检查与治疗,以供同道们参考。 The disease is a worldwide distribution of young and middle-aged diseases, rare in children. It is characterized by the involvement of elastic aorta, progressive vasculitis become aggravated, until the lumen occlusion. Due to the different parts of the affected vessels, clinical complex, changing, elusive performance, such as some of the early ischemic symptoms, it is easy to misdiagnose as neurological disorders or connective tissue diseases, leading to delays in treatment for This article focuses on the clinical manifestations of the disease, laboratory tests and treatment for fellow reference.