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报告小儿肾上腺皮质腺癌７例，其中功能性６例，非功能性１例。性征异常１例，其余表现为糖皮质激素和性激素混合性分泌紊乱综合征。细胞形态学改变与生物学行为有时并不一致，会造成延误诊断。２４小时尿１７－ＫＳ超过６９．４μｍｏｌ，大剂量地塞米松抑制试验不能被抑制，肿瘤直径＞５ｃｍ，边缘不规则，密度不均匀，应考虑肾上腺皮质恶性肿瘤。早期肿瘤切除，配合联合化疗、放疗以提高疗效。
Seven cases of pediatric adrenocortical adenocarcinoma were reported, including 6 cases of functional and 1 case of non-functional. 1 case of abnormal sexual characteristics, the remaining performance of glucocorticoid and sex hormone mixed secretion syndrome. Sometimes morphological changes and biological behavior are not consistent, will result in delayed diagnosis. 24-hour urine 17-KS more than 69.4μmol, high-dose dexamethasone suppression test can not be suppressed, the tumor diameter> 5cm, irregular edges, uneven density, adrenocortical malignancy should be considered. Early tumor resection, with the combination of chemotherapy, radiotherapy to improve efficacy.