白塞氏病(Behcet’氏病)是1937年Behcet氏首次描述和报道,相继世界文献有较多报告,国内亦有少数神经白塞氏病的病例报道,但尚未见到病理报告。现将我院一例尸检病例结合临床报道如下。病例介绍患者朱××,女性,41岁。自1981年10月开始经常有低烧伴皮肤红斑,和具有压痛的皮下结节以及鼻腔粘膜溃疡等。曾按“风湿热”给予激素治疗。同年12月在激素减量过程中,出现左眼视物模糊,头晕,复视,去医院检查发现左眼底视网膜有瘀血斑、玻璃体混浊,诊断为“葡萄膜炎”,又给激素治疗效果不显。至1983年2月12日(即入院前20天)突然出现头晕伴有恶心呕吐、耳鸣、复视加重,逐 Behcet’s disease (Behcet’s disease) was first described and reported by Behcet’s in 1937. There have been more reports in successive world literature. There are also a few cases of neurobehavior in China, but no pathological reports have been reported yet. Now a case of autopsy in our hospital combined with clinical reports are as follows. Case description Zhu × ×, female, 41 years old. Since October 1981 often have low-grade fever with skin erythema, and subcutaneous nodules with tenderness and nasal mucosal ulcers and so on. According to “rheumatic fever” to give hormone therapy. In the same year in December in the process of reducing hormone, the left eye appears blurred vision, dizziness, diplopia, go to the hospital to check the left fundus retinal bleeding stasis, vitreous opacity, diagnosed as “uveitis”, giving hormone treatment effect Not significant. To February 12, 1983 (ie 20 days before admission) suddenly with dizziness accompanied by nausea and vomiting, tinnitus, diplopia increased, by