积水性无脑畸形是脑先天畸形病变之一，主要表现为大脑结构大部丧失，颅内形成一含脑脊液的巨大囊腔。CT对该病的诊断很有价值，能清楚显示病变的病理特征。由于其他一些颅内病变也可形成含脑脊液囊性区，故认识积水性无脑畸形的CT表现对于该病的诊断和鉴别至关重要。本文报告2 Accumulation of water-free anencephaly is one of the congenital malformations of the brain, the main manifestation of most of the loss of brain structure, the formation of a cerebrospinal fluid in the intracranial giant cysts. CT diagnosis of the disease is valuable, can clearly show the pathological features of the lesion. As some other intracranial lesions can also be formed with cerebrospinal fluid cystic area, so understanding of hydrocephalus anencephaly CT findings for the diagnosis and identification of the disease is essential. This paper reports 2