I型自身免疫性多内分泌腺病(APG I)亦称为自身免疫性多内分泌腺病-念珠菌病-外胚层营养不良或自身免疫性多内分泌腺衰竭综合征。最早的报告是在1956年,指病人存在甲状旁腺功能减退,肾上腺功能低下和粘膜皮肤念珠菌感染。此后,又发现有许多其它内分泌腺病的病状。本文作者报道过去12年间确诊的9例APG I病人,年龄14～48岁,均接受过内分泌检查,并做过上腹部超声检查或腹部的CT扫 Type I autoimmune polyendocrinopathy (APG I) is also known as autoimmune polyendocrinopathies-candidiasis-ectodermal dystrophy or autoimmune polyendrine gland failure syndrome. The earliest report was in 1956, referring to patients with hypoparathyroidism, adrenal insufficiency and mucocutaneous candidiasis. Since then, many other endocrine conditions have been found. The authors report that 9 patients with APG I diagnosed in the past 12 years, aged 14 to 48 years, had undergone endocrine examinations and underwent abdominal ultrasonography or abdominal CT scan