视-隔发育不全(SOD)是脑叶型前脑畸形的轻型,合并视神经发育不良和透明隔缺损,由DeMorsier于1956年命名[1],故又称DeMorsier综合征。我们遇到1例,现报道如下。患儿男,12个月。出生后即双眼保持内下注视,于2005年12月4日来我科就诊。患儿自出生以来对眼前放置的物体没有反应,对 Optic-septal hypoplasia (SOD) is a type of brain lobar forebrain deformity with mild optic neurodevelopment and translucent defects, deMorsier named in 1956 [1], it is also known as DeMorsier syndrome. We encountered a case, are reported below. Children male, 12 months. After birth, both eyes remain under the watch, on December 4, 2005 to our department. The child has no response to the object placed in front of him since birth