虹膜角膜内皮综合征是一种少见的眼病,它包括三个主要临床类型,即原发进性行性虹膜萎缩,Chandler氏综合征和虹膜痣综合征。我院从1979～1989年共遇到9例现报告如下。临床资料本文9例中男性2例,女性7例,年龄最小15岁、最大42岁,双眼发病3例,单眼发病6例,共12眼。9例患者中有2例为原发性进行性虹膜萎缩,7例为虹膜痣综合征。12眼中有11眼继发青光眼,除3例4眼 Iris Corneal endothelial syndrome is a rare ocular disease that includes three major clinical categories, primary progressive iris atrophy, Chandler’s syndrome and iris nevus syndrome. Our hospital from 1979 to 1989, a total of 9 cases are reported as follows. Clinical data of 9 cases, 2 males and 7 females, the youngest 15 years old, maximum 42 years old, 3 cases of binocular disease, monocular disease in 6 cases, a total of 12 eyes. Two of the nine patients had primary progressive iris atrophy and seven had iris nevus syndrome. 11 of 12 eyes had secondary glaucoma, except 3 of 4 eyes