分析经手术及病理证实的儿童椎管内肿瘤133例。自胚胎残余组织发生的肿瘤占57.9%,其中上皮样囊肿和皮样囊肿居多,临床以进行性肢体力弱及括约肌障碍多见,合并皮毛窦及脊柱侧弯畸形等亦较多。74.3%的 X 线平片有骨质改变,认为细致的临床检察和加强对可疑者的辅助检查对确诊很有帮助。大多数病例行大部至全切除。能随诊到的病例中,5年生存率为49.3%。指出术中不损伤脊柱小关节,可减少术后脊柱畸形。本病预后较成人差。 Analysis of 133 cases of spinal canal tumors confirmed by surgery and pathology. Tumors from the residual tissue of embryos accounted for 57.9%, of which epithelial cysts and dermoid cysts were mostly clinically progressive weak limbs and sphincter dysfunction more common with sinus and scoliosis malformations are also more. 74.3% of X-ray films have bone changes, that the detailed clinical examination and to strengthen the suspicious auxiliary examination is helpful. Most of the cases line to the total resection. Among the cases that can be followed up, the 5-year survival rate was 49.3%. Pointed out that surgery does not damage the spine facet joint, can reduce postoperative spinal deformity. The prognosis of the disease worse than adults.