病例资料:患者,女,14岁。主因间断腹痛20d,加重1周入院。查体:精神反应可,面部鼻唇沟区多发皮肤皮脂腺瘤,心肺正常,腹部稍胀,左上腹可扪及一8cm×10cm大肿物,压痛明显,边缘欠清晰,肾区叩击痛(+)。既往体健。实验室检查血、尿常规无异常。B超在左上腹脾、肾间可探及9.8cm×8.0cm Case Information: Patient, female, 14 years old. The main reason for intermittent abdominal pain 20d, increased 1 week admission. Physical examination: mental reaction can be, facial nasolabial area multiple sebaceous tumors of the skin, normal lung and heart, abdominal swollen, left upper abdomen palpable and a large tumor of 8cm × 10cm, tenderness, the edge is not clear, the perineural area percussion pain +). Past physical health. Laboratory tests blood, urine no abnormalities. B-in the left upper quadrant spleen, renal exploration and 9.8cm × 8.0cm