运动神经元病系一组累及脊髓前角细胞和/或脑干(特别是延髓运动神经核)的慢性进行性变性损害,因其主要表现为运动系统受损,故又称核性肌萎缩或运动系统疾病:包括进行性脊髓性肌萎缩症、肌萎缩性侧索硬化症、婴儿型脊髓性肌萎缩症、家族性进行性脊髓性肌萎缩症、进行性球麻痹和原发性侧索硬化症等。近年来发现本病并非 Motor neuron disease is a group of chronic progressive degenerative lesions involving the spinal cord anterior horn cells and / or the brainstem (especially the medulla oblongata), which are also known as corpus mythiasis or Motor system diseases: progressive spinal muscular atrophy, amyotrophic lateral sclerosis, infantile spinal muscular atrophy, familial progressive spinal muscular atrophy, progressive palsy and primary lateral sclerosis Disease and so on. In recent years found that the disease is not