经CT诊断13例神经皮肤综合征,其中结节性硬化6例;神经纤维瘤病6例;颅面血管瘤综合征1例。结节性硬化CT表现为两侧脑室室管膜下脑室周围或脑实质内单发或多发之钙化结节,值得注意的是这些颅内钙化灶可可以先于面部皮脂腺瘤出现之前。神经纤维瘤病可合并脑膜瘤 CT diagnosis of 13 cases of neurodermal syndrome, including tuberous sclerosis in 6 cases; 6 cases of neurofibromatosis; 1 case of craniofacial hemangioma syndrome. Tuberous sclerosis CT manifests as solitary or multiple calcified nodules around the periventricular or intraparenchymal subventricular ducts in the bilateral ventricles. It is noteworthy that these intracranial calcifications may precede the appearance of facial sebaceous adenomas. Neurofibromatosis can be associated with meningioma