我院 1 980年～ 1 996年收治肝豆状核变性病人 52例 ,其中伴贫血者 2 0例 ,现分析报道如下。1　临床资料1 .1　一般资料　男 1 4例 ,女 6例。就诊时年龄 6～ 8岁 1 1例 ,9～ 1 1岁 4例 ,1 2～ 1 4岁 5例。病史最长 5年 ,最短 1 0余天。 8例同胞兄妹中有阳性发现 ,3例近亲中有阳 Our hospital from 1980 to 1996 in the treatment of hepatolenticular degeneration in 52 patients, of which 20 cases with anemia, are now analyzed as reported below. 1 clinical data 1.1 general information male 14 cases, female 6 cases. At the time of treatment, there were 11 cases aged 6 to 8 years old, 4 cases aged 9 to 11 years and 5 cases between 12 and 14 years old. The longest history of 5 years, the shortest more than 10 days. 8 cases of siblings have positive findings, 3 cases of cousins ​​have positive