永存左上腔静脉大多引流至冠状窦。直接引流至左房者罕见,常伴冠状窦缺如。本文报道二例左上腔静脉直接引流至左房且伴正常冠状窦。例1 2岁的法乐四联症患儿。在外科修补术前曾作心导管检查。血流动力学检查提示非限制性室间隔缺损(右和左室峰压为 Most of the left ventricular superficial drainage to the coronary sinus. Direct drainage to the left atrium rare, often accompanied by coronary sinus missing. This article reports two cases of left superior vena cava direct drainage to the left atrium and with normal coronary sinus. Example 1 A 2-year-old child with tetralogy of Fallot. Cardiac catheterization was performed prior to surgical repair. Hemodynamic findings suggest unrestricted ventricular septal defects (right and left ventricular peak pressures)