痣样基底细胞癌综合征在临床上罕见 ,以多发性颌骨角化囊肿为主要临床表现 ,同时伴有多种其他表现 ,易误诊误治。现将我院近日收治的 1例典型病例报道如下。1　病例资料患者 ,男 ,4 5岁 ,以“右侧面部反复肿胀伴不适 1年余”收住院。患者诉 1998年初因“双侧上颌窦炎症”在其它 Mole-like basal cell carcinoma syndrome is clinically rare, with multiple jaw keratocyst as the main clinical manifestations, accompanied by a variety of other manifestations, misdiagnosis and mistreatment. Now in our hospital recently treated a typical case reported below. 1 case data patients, male, 45 years old, with “the right side of the face repeatedly swelling with discomfort for more than 1 year” admitted to hospital. Patient v. Early 1998 due to “bilateral maxillary sinusitis” among others